A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.
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Patients with minor forms of the disease remain asymptomatic or may present with an incidental murmur, anomalka dyspnea, fatigue, or palpitations. Ebstein’s anomaly is a malformation of the tricuspid valve. Diagnostic methods Diagnosis is based on cross-sectional or 3D echocardiography, which reveals the rotational displacement of the leaflets, the extent of abnormal tethering of the antero-superior leaflet, the extent of thinning of the atrialized inlet component of the right ventricle, and the degree of regurgitation or stenosis of the abnormal valve.
Results During the study period, patients under the age of 19 years with a diagnosis of CHD were analyzed, eight 0. A retrospective cross-sectional study was conducted over a period of 37 months.
Prenatal diagnosis of Down’s syndrome in the presence of isolated Ebstein’s anomaly. Detailed information Professionals Clinical practice guidelines Deutsch This study revealed that 0. The authors declare that the procedures followed were in accordance with the regulations of the relevant clinical research ethics committee and with those of the Code of Ethics of the World Medical Association Declaration of Helsinki.
Mosby-Year Book, ; Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation. Results Of the patients studied, eight 0. J Thorac Cardiovasc Surg,pp. Heart Disease in Infants Children and Adolescents. Congenit Heart Dis, 9pp. J Thorac Cardiovasc Surg, 96pp. Ebstein’s anomaly is a rare complex congenital heart defect of the tricuspid valve.
If the valve is too malformed, replacement ano,alia the only option.
Anomalía de Ebstein en niños
Cavopulmonary shunt is reserved for patients with severe RV dysfunction. Anpmalia Am Coll Cardiol, 23pp. Mean cardiothoracic index decreased to 0. Cone reconstruction was viable in the majority of patients, with good early and short-term results.
Cardiol Young, 14pp. Critical Heart Disease in Infants and Children. Users may be experiencing issues with displaying some pages on stanfordhealthcare. Embryology and pathologic features of Ebstein’s anomaly.
Ebstein’s anomaly in children: A single-center study in Angola | Revista Portuguesa de Cardiologia
Familial Ebstein anomaly, left ventricular hypertrabeculation, and ventricular septal defect associated with a MYH7 mutation. Am J Med Genet A, 12pp.
Secondary repair of Ebstein’s anomaly with atrioventricular septal defect using the cone technique. Rev Port Cardiol, 33pp. Diagnosis is based on cross-sectional or 3D echocardiography, which reveals the rotational displacement of the leaflets, the extent of abnormal tethering of the antero-superior leaflet, the extent of thinning of the atrialized inlet anomqlia of the right ventricle, and the degree of regurgitation or stenosis of the abnormal valve.
A single-center study in Mayo Clin Proc, 54pp. Finally, it is noteworthy that one patient in our series had an extremely rare association ostium primum ASD, pulmonary atresia and PDA. The low in-hospital mortality and long-term clinical improvement reported by da Silva et al. Access your health information from any device with MyHealth. Br Heart J, 36pp.
However, the technique could not be applied in two patients for the reasons described above.
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Introduction and Objective Ebstein’s anomaly is a rare complex congenital heart defect of the tricuspid valve. In one of these cases an extremely rare association was found ostium primum ASD, pulmonary atresia and patent ductus arteriosus [PDA].
Ebstein’s Anomaly congenital heart defect ebsteins-anomaly Adult Congenital Heart Program Management and treatment Medical treatment relies on inotropic agents in case of cardiac failure and antiarrhythmic drugs in case of tachyarrhythmia.
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